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中华肺部疾病杂志(电子版) ›› 2019, Vol. 12 ›› Issue (04) : 531 -533. doi: 10.3877/cma.j.issn.1674-6902.2019.04.032

病例报告

原发性纤毛运动障碍一例
杨俊俊1, 徐兴祥1,(), 王正东1, 邹晶2   
  1. 1. 225000 江苏,苏北人民医院呼吸与危重症医学科
    2. 434000 湖北,荆州市第一人民医院呼吸内科
  • 收稿日期:2019-03-25 出版日期:2019-08-20
  • 通信作者: 徐兴祥

One case report of primary ciliary dyskinesia

Junjun Yang1, Xingxiang Xu1(), Zhengdong Wang1   

  • Received:2019-03-25 Published:2019-08-20
  • Corresponding author: Xingxiang Xu
引用本文:

杨俊俊, 徐兴祥, 王正东, 邹晶. 原发性纤毛运动障碍一例[J]. 中华肺部疾病杂志(电子版), 2019, 12(04): 531-533.

Junjun Yang, Xingxiang Xu, Zhengdong Wang. One case report of primary ciliary dyskinesia[J]. Chinese Journal of Lung Diseases(Electronic Edition), 2019, 12(04): 531-533.

图1 患者杵状指、杵状趾改变
图2 鼻窦CT(2011年)显示鼻腔黏膜增厚,单组或多组鼻窦炎性改变,窦壁骨质增生硬化,伴鼻息肉改变
图3 胸部HRCT示:两肺纹理增多,两肺下叶见网格影及点状、磨玻璃样稍高密度影,右肺中叶、两下肺病变见多发系轨道征,部分支气管囊状扩张、腔内见小液平
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